An 11-month-old cyanotic infant presented to pediatric cardiology outpatient clinic with respiratory distress and oxygen saturation of 70 % on room air. Chest radiograph revealed dextrocardia and with a tortuous tubular opacity (Fig. 1A) seen in left lower lung field. Subsequently transthoracic echocardiography was performed which revealed dextrocardia with complete atrioventricular septal defect and total anomalous pulmonary venous connection (TAPVC).