Auriculocondylar syndrome (ACS; MIM 602483), also known as “question-mark ear syndrome” or “dysgnathia complex,” is a rare autosomal dominant craniofacial malformation syndrome. It is characterized by variable mandibular anomalies ranging from mild micrognathia to severe mandibular hypoplasia, cleft palate, and a distinctive auricular malformation consisting of lobule–helix separation, producing the “question-mark ear” (QME) appearance (Figs. 1, 2) [1–3]. Additional commonly reported features in…