CCTGA is characterised by combined atrioventricular (AV) and ventriculoarterial (VA) discordance [1]. Systemic and pulmonary veins typically connect to their appropriate lateralised atria (normal connections). The morphologically right ventricle (mRV) connects to the left atria and an anterior left sided aorta. Consequently, there is a systemic mRV and the tricuspid valve guards the left sided AV junction, while the mitral valve is at the right-sided junction (Fig. 1a). This mirror-imaged ventri…